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GSS Prion Disease: Understanding Gerstmann-Sträussler-Scheinker Syndrome

GSS Prion Disease: Understanding Gerstmann-Sträussler-Scheinker Syndrome Gerstmann-Sträussler-Scheinker syndrome (GSS) is a rare, inherited, and invariably fatal neurodegenerative disorder classified as a prion disease. Unlike the more commonly known Creutzfeldt-Jakob disease (CJD), GSS is characterized by a slower progression and a distinct clinical presentation. Understanding the intricacies of this disease, from its genetic basis to its…

Understanding GSS: A Comprehensive Guide to Gerstmann-Sträussler-Scheinker Syndrome
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Understanding GSS: A Comprehensive Guide to Gerstmann-Sträussler-Scheinker Syndrome

What is Gerstmann-Sträussler-Scheinker Syndrome (GSS)? Gerstmann-Sträussler-Scheinker syndrome (GSS) is a rare, inherited, and invariably fatal neurodegenerative disorder. It’s classified as a prion disease, a group of conditions caused by misfolded proteins that accumulate in the brain, leading to progressive neurological damage. Unlike some prion diseases like Creutzfeldt-Jakob disease (CJD), GSS typically has a later onset…