Understanding GSS: A Comprehensive Guide to Gerstmann-Sträussler-Scheinker Syndrome
What is Gerstmann-Sträussler-Scheinker Syndrome (GSS)? Gerstmann-Sträussler-Scheinker syndrome (GSS) is a rare, inherited, and invariably fatal neurodegenerative disorder. It’s classified as a prion disease, a group of conditions caused by misfolded proteins that accumulate in the brain, leading to progressive neurological damage. Unlike some prion diseases like Creutzfeldt-Jakob disease (CJD), GSS typically has a later onset…